The retina is the coating of the back of the eye made of specialized cells that process light and colour for us to see. Uncontrolled growth of retinal cells due to a change in a gene, known as the retinoblastoma (RB) gene, causes retinoblastoma (pronounced ret'-n-oh-bla-stoh'-muh).
Retinoblastoma is a rare form of cancer, affecting 1 in 15,000 live births. Retinoblastoma is considered a childhood cancer since it mostly affects children less than 5 years of age. There seems to be an equal chance of the condition occurring in either eye, in either boys or girls, and regardless of race. About 75% of cases occur in one eye, and about 25% of cases occur in both eyes.